Emily's Disease

class try's to figure out Emilyl's disease

could Emily have sickle cell anemia?

I think Emily might have sickle cell anemia because when I looked at the jigsaw puzzle it told me the symptoms. A lot of the symptoms of sickle cell anemia Emily has. I also thought this because sickle cell anemia happens when Red Blood Cell's get stuck in your blood vessels so I used our Red Blood Cell work sheet to help me. Sickle Cell Anemia affects two systems, the Respiratory and the Circulatory.

What is Sickle Cell Anemia?

Sickle Cell Anemia is when the Red Blood Cells form into a crescent moon and get stuck in blood vessels. Two systems that are affected are the Circulatory system and the Respiratory system. The Circulatory system is affected because Emily has pain in her chest and that pain is caused by the Red Blood Cells getting stuck in the blood vessels. This makes it hard to breathe and could also cause dizziness. It also affects the Respiratory system because when you have pain in your chest it could cause damage to your lungs which could lead to having trouble breathing.

treatment for Sickle Cell Anemia

Treatment

The goals of treating sickle cell disease are to prevent or relieve pain; prevent infections, organ damage, and strokes; treat anemia; and control complications.

Some doctors and clinics specialize in treating people who have sickle cell disease. Hematologists specialize in treating adults and children who have blood diseases and disorders.

Treating Pain

Mild pain is often treated with over-the-counter medicine and heating pads. Severe pain may need to be treated in a hospital. The usual treatments for acute (short-term) pain crises are fluids and pain-controlling medicines. Fluids help prevent dehydration, a condition in which the body doesn't have enough fluids. Fluids are given either by mouth or through a vein.

Common medicines used to treat pain crises include acetaminophen, nonsteroidal anti-inflammatory drugs (NSAIDs), and narcotics. Treatment for mild to moderate pain usually begins with NSAIDs or acetaminophen. If pain continues, a narcotic may be needed. Moderate to severe pain is often treated with narcotics. The narcotic may be used alone or with NSAIDs or acetaminophen.

Preventing Pain

Those with more severe sickle cell anemia may benefit from daily administration of a medicine called hydroxyurea. This medicine may help reduce the number of painful crises. Hydroxyurea is used to prevent painful crises, not to treat them when they occur.

Preventing Infection

Bacterial infections can be a major complication of sickle cell disease, but often they can be prevented or treated. If a child who has sickle cell disease shows early signs of an infection, such as a fever, difficulty breathing, or localized bone pain, treatment should be given right away.

To prevent infections in babies and young children, treatments include:

  • Daily doses of penicillin. Treatment may begin as early as 2 months of age and continue until the child is at least 5 years old.
  • All routine vaccinations (including a yearly flu shot), plus vaccination(s) against streptococcus pneumonia.

Adults who have sickle cell disease should also receive flu shots every year and get vaccinated against pneumococcal infections. Both adults and children are at risk for a variety of infections, such as pneumonia and bone infections. They should be examined whenever they experience fevers, since early diagnosis and treatment result in better outcomes.

Preventing Complications

Complications from sickle cell disease can include gallstones, lung crises (acute chest syndrome), pulmonary hypertension, stroke, leg ulcers that don't heal, and eye damage.

Blood transfusions are commonly used to treat worsening anemia and sickle cell complications. Most patients with sickle cell disease have at least occasional blood transfusions. Patients with severe complications–such as stroke and acute chest syndrome–may require months or years of regular transfusions every three to four weeks to prevent ongoing damage.

Hydroxyurea treatment may be helpful in reducing crises and the need for transfusions.

People with sickle cell disease should have regular checkups to detect eye damage. And a simple ultrasound test of the head can identify children at high risk for strokes.

Sickle Cell Anemia